儿科炎性肌纤维母细胞瘤:诊断、多学科管理和手术策略方面的挑战

IF 0.5 Q4 PEDIATRICS
Izchel Valdez García, Alejandro Solano Gutierrez, Sofia Brenes Guzmán, Brenda Aguilar Viveros
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引用次数: 0

摘要

炎性肌纤维母细胞瘤是一种罕见但影响深远的疾病,尤其是在儿童群体中。本病例报告揭示了诊断和治疗儿童炎性肌纤维母细胞瘤的复杂挑战,强调了跨学科合作对制定有效治疗策略的重要性。值得注意的是,手术方式的选择对复发和转移的风险有着至关重要的影响,与支气管镜下的楔形切除术相比,支气管切开术、肺叶切除术和肺切除术等广泛切除术的复发率明显降低。我们介绍了一例 3 岁女孩的病例,她患有进行性无痰咳嗽,偶尔伴有咯血和肺炎,持续一年,继发于炎性肌纤维母细胞瘤,经支气管切开术切除后效果极佳。鉴于这种疾病在儿科患者中极为罕见,持续的研究工作和集体专业知识的积累至关重要。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Inflammatory myofibroblastic tumor in pediatric patients: challenges in diagnosis, multidisciplinary management, and surgical strategies
Inflammatory myofibroblastic tumor is a rare yet profoundly impactful condition, particularly within the pediatric population. This case report illuminates the intricate challenges of diagnosing and managing inflammatory myofibroblastic tumors in children, underscoring the importance of interdisciplinary collaboration in formulating effective treatment strategies. Notably, the choice of surgical approach holds a paramount influence on the risk of recurrence and metastasis, with wide resection with bronchotomy, lobectomy, and pneumonectomy demonstrating significantly diminished recurrence rates compared to wedge resection in bronchoscopic removal. We present the case of a 3-year-old girl with a progressive, nonproductive cough, occasionally accompanied by episodes of hemoptysis and pneumonia for a year, secondary to an inflammatory myofibroblastic tumor that was removed by bronchotomy with excellent results. Given the extraordinary rarity of this disease in pediatric patients, ongoing research endeavors and the accumulation of collective expertise are paramount.
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来源期刊
自引率
0.00%
发文量
32
审稿时长
9 weeks
期刊介绍: The Gazette is the official journal of the Egyptian Pediatric Association. The main purpose of the Gazette is to provide a place for the publication of high-quality papers documenting recent advances and new developments in both pediatrics and pediatric surgery in clinical and experimental settings. An equally important purpose of the Gazette is to publish local and regional issues related to children and child care. The Gazette welcomes original papers, review articles, case reports and short communications as well as short technical reports. Papers submitted to the Gazette are peer-reviewed by a large review board. The Gazette also offers CME quizzes, credits for which can be claimed from either the EPA website or the EPA headquarters. Fields of interest: all aspects of pediatrics, pediatric surgery, child health and child care. The Gazette complies with the Uniform Requirements for Manuscripts submitted to biomedical journals as recommended by the International Committee of Medical Journal Editors (ICMJE).
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