Judith Monserrat Corona-Herrera, uis Asdruval Zepeda-Gutiérrez, O. E. Falcon-Antonio, A. Barrera-Godínez, Silvia Méndez Flores, J. Domínguez-Cherit
{"title":"从黄斑淋巴细胞性动脉炎到皮肤结节性多动脉炎:同一种疾病的谱系?两个临床表现相同但组织病理学结果不同的病例","authors":"Judith Monserrat Corona-Herrera, uis Asdruval Zepeda-Gutiérrez, O. E. Falcon-Antonio, A. Barrera-Godínez, Silvia Méndez Flores, J. Domínguez-Cherit","doi":"10.7241/ourd.20241.15","DOIUrl":null,"url":null,"abstract":"Macular lymphocytic arteritis (MLA) is a type of indolent cutaneous vasculitis that affects small to medium-sized blood vessels. Histopathologically, it is characterized by a predominantly lymphocytic leukocytic infiltrate (unlike polyarteritis nodosa, in which neutrophils predominate) in the blood vessels of the deep dermis and superficial hypodermis. The disease mainly affects females (17:3), with a mean age of forty years. In general, this entity is considered benign with a variable clinical presentation. The importance of knowing this entity lies in the fact that the pathological findings are discordant with the clinic and an erroneous diagnosis may lead to unnecessary treatments. This vasculitis usually has a benign course and no progression to systemic disease. Herein, we present two cases of this rare vasculitis. Key words: Macular lymphocytic arteritis, Cutaneous polyarteritis nodosa, Vasculitis, Systemic lupus erythematosus","PeriodicalId":494108,"journal":{"name":"Our Dermatology Online","volume":"94 2","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2024-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"From macular lymphocytic arteritis to cutaneous polyarteritis nodosa: A spectrum of the same disease? Two cases of the same clinical presentation yet different histopathological findings\",\"authors\":\"Judith Monserrat Corona-Herrera, uis Asdruval Zepeda-Gutiérrez, O. E. Falcon-Antonio, A. Barrera-Godínez, Silvia Méndez Flores, J. Domínguez-Cherit\",\"doi\":\"10.7241/ourd.20241.15\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Macular lymphocytic arteritis (MLA) is a type of indolent cutaneous vasculitis that affects small to medium-sized blood vessels. Histopathologically, it is characterized by a predominantly lymphocytic leukocytic infiltrate (unlike polyarteritis nodosa, in which neutrophils predominate) in the blood vessels of the deep dermis and superficial hypodermis. The disease mainly affects females (17:3), with a mean age of forty years. In general, this entity is considered benign with a variable clinical presentation. The importance of knowing this entity lies in the fact that the pathological findings are discordant with the clinic and an erroneous diagnosis may lead to unnecessary treatments. This vasculitis usually has a benign course and no progression to systemic disease. Herein, we present two cases of this rare vasculitis. Key words: Macular lymphocytic arteritis, Cutaneous polyarteritis nodosa, Vasculitis, Systemic lupus erythematosus\",\"PeriodicalId\":494108,\"journal\":{\"name\":\"Our Dermatology Online\",\"volume\":\"94 2\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2024-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Our Dermatology Online\",\"FirstCategoryId\":\"0\",\"ListUrlMain\":\"https://doi.org/10.7241/ourd.20241.15\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Our Dermatology Online","FirstCategoryId":"0","ListUrlMain":"https://doi.org/10.7241/ourd.20241.15","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
From macular lymphocytic arteritis to cutaneous polyarteritis nodosa: A spectrum of the same disease? Two cases of the same clinical presentation yet different histopathological findings
Macular lymphocytic arteritis (MLA) is a type of indolent cutaneous vasculitis that affects small to medium-sized blood vessels. Histopathologically, it is characterized by a predominantly lymphocytic leukocytic infiltrate (unlike polyarteritis nodosa, in which neutrophils predominate) in the blood vessels of the deep dermis and superficial hypodermis. The disease mainly affects females (17:3), with a mean age of forty years. In general, this entity is considered benign with a variable clinical presentation. The importance of knowing this entity lies in the fact that the pathological findings are discordant with the clinic and an erroneous diagnosis may lead to unnecessary treatments. This vasculitis usually has a benign course and no progression to systemic disease. Herein, we present two cases of this rare vasculitis. Key words: Macular lymphocytic arteritis, Cutaneous polyarteritis nodosa, Vasculitis, Systemic lupus erythematosus