Sinovitis villonodular de la articulación coxofemoral, presentación atípica: reporte de caso y revisión de la literatura

Introduction

Pigmented villonodular synovitis is an uncommon clinical condition, with a higher incidence in women of 3:1, and an age of presentation between 20-40 years old. The hip is an uncommon site, being involved in only 15% of all cases.

Case report

A 47 year-old male 47 years with a history of 10 years onset, characterised by limited range of movement, pain associated with increased volume and shortening of pelvic limb. Imaging studies showed destruction of hip joint and extension to the pelvis. The histopathology reported pigmented villonodular synovitis. Treatment included a left outer hemipelvectomy.

Conclusions

The presentation of a diffuse pigmented villonodular synovitis hip has a low incidence and its locally aggressive behaviour makes it necessary to perform differential diagnoses to include malignancies. The standard treatment is surgical.