儿童罗素-银综合征(RSS)接受先天性白内障手术:1例报告

IF 0.6 Q3 ANESTHESIOLOGY

Egyptian Journal of Anaesthesia Pub Date : 2023-10-03 DOI:10.1080/11101849.2023.2262187

Dina Hatem Ahmed, Mo’men Mostafa Youssef Makkey, Medhat Sayed Radwan, Ahmed Ismaiel Abdel Sabour

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引用次数: 0

摘要

罗素-银综合征(russel - silver syndrome, RSS)是一种罕见但众所周知的印记疾病，其主要特征是出生后发育障碍和特发性宫内生长迟缓(IUGR)，倒三角脸和突出的前额伴相对大头畸形，这将其与特发性宫内生长迟缓和其他原因的出生后生长障碍区分出来。由于下颌发育不全导致牙关咬合和牙套使用困难，导致围手术期患者插管困难的病例报道很少。

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A child with Russell–Silver syndrome (RSS) undergoing surgery for congenital cataract: Case report

Background Russell–Silver syndrome (RSS) is an uncommon but well-known imprinting condition primarily characterized by postnatal development failure and idiopathic intrauterine growth retardation (IUGR) and an inverted triangular face and a prominent forehead with relative macrocephaly that distinguish it from idiopathic IUGR and other causes of postnatal growth failure. Few case reports of RSS with cleft palate have been published and those who have perioperative issue such difficult intubation owing to trismus and difficulty to use a mouthpiece due to mandibular development failure.

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来源期刊

Egyptian Journal of Anaesthesia Medicine-Anesthesiology and Pain Medicine

CiteScore

0.90

自引率

0.00%

发文量