正中弓状韧带综合征(邓巴综合征)是一个多学科问题。临床观察及文献参考

O.I. Dorovskaya, Ya.L. Manakova, N.L. Tov, D.L. Nepomnyashchikh, K.A. Brezhneva, L.A. Kharlamova
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引用次数: 0

摘要

介绍。中弓韧带综合征(Median arcuate ligament syndrome, MALS, Dunbar syndrome)是一种罕见的血管压迫综合征,是由膈正中弓韧带在血管外压迫腹腔干(CT)和腹腔丛引起的,是引起慢性腹腔缺血和神经性疼痛综合征的原因之一。临床观察。女性,36岁,因腹痛中度,腹泻每天10次,过去一年体重减轻11公斤而住院。排除炎性肠病、麸质肠病、小肠淋巴瘤、吸收不良综合征、内分泌系统病理。进行腹部高分辨率计算机断层扫描(HRCT)血管造影。CT表现为高达90%的血管外压迫,中间弓状韧带增厚,形成u形变形。腹腔镜减压手术同时行腔内血管成形术,压迫减轻,临床症状消失。18个月后,临床改善持续,腹泻消失。HRCT血管造影和超声双工检查(USDE)显示CT系统血流充足。在随访期间,患者有中度神经性疼痛和需要适当纠正的焦虑和抑郁障碍。结论。肌萎缩侧索硬化症的诊断和治疗方法应以患者为中心,并需要一个专家团队的参与。腹腔镜减压是一种有效的治疗方法,可以立即缓解症状。干预效果可通过HRCT血管造影和USDE(两种方法相辅相成)评估。神经性疼痛综合征和焦虑抑郁障碍的矫正对提高患者的生活质量具有重要意义。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
MEDIAN ARCUATE LIGAMENT SYNDROME (DUNBAR SYNDROME) AS A MULTIDISCIPLINARY PROBLEM. CLINICAL OBSERVATION AND LITERATURE REFERENCE
Introduction. Median arcuate ligament syndrome (MALS, Dunbar syndrome) is a rare vascular compression syndrome caused by extravascular compression of the celiac trunk (CT) and celiac plexus by the median arcuate ligament of the diaphragm and is one of the causes of chronic abdominal ischemia and neuropathic pain syndrome. Clinical observation. A woman, 36 years old, was hospitalized with complaints of abdominal pain of moderate intensity, diarrhea up to 10 times a day, weight loss of 11 kg over the past year. Inflammatory bowel disease, gluten enteropathy, lymphoma of the small intestine, malabsorption syndrome, pathology of the endocrine system was excluded. Abdominal high-resolution computed tomography (HRCT) angiography was performed. Signs of extravascular compression of CT up to 90% with a thickened median arcuate ligament with the formation of a U-shaped deformation were revealed. Laparoscopic decompression surgery was performed with simultaneous transluminal angioplasty, which led to a decrease in compression and disappearance of clinical symptoms. After 18 months, clinical improvement persisted, diarrhea disappeared. HRCT angiography and ultrasound duplex examination (USDE) showed sufficient blood flow in the CT system. During the follow-up period, the patient had moderate neuropathic pain and anxiety and depressive disorders requiring appropriate correction. Conclusion. The diagnostic and therapeutic approach to MALS should be patient-centered and requires the involvement of a team of specialists. Laparoscopic decompression is an effective treatment and can provide immediate symptoms relief. The results of the intervention can be assessed by HRCT angiography and USDE (methods supplementing each other). Correction of neuropathic pain syndrome and anxiety-depressive disorder is of great importance for improving the patient's quality of life.
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