An Unusual Presentation of Penile Kaposi’s Sarcoma in an HIV-Negative Patient with a Circumcised Penis

Kaposi sarcoma (KS) is a multifocal hemorrhagic sarcoma that occurs mainly in the extremities. KS limited to the penis is rare and usually associated with acquired immunodeficiency syndrome (AIDS). The clinical presentations and courses of KS in the penis demonstrate variability, with limited reports of non-HIV-related primary KS. Herein, we present the case of a 27-year-old male patient with a classic form of KS who had a primary glans penile macular lesion. In more detailed evaluations, we found no evidence of immunosuppression or systemic involvement of the disease. There was no recurrence in the patient who underwent surgical excision, and he was followed up.