Orbito-Temporal Hamartoma in a Newborn

We report the case of a male newborn, eleven days old, born in a context of dystocic delivery, but without notion of resuscitation or oxygen therapy. He was referred for protrusion of the left eyeball observed at birth. The right eye examination was normal. In the left eye we found a congenital, axile, irreducible and inflammatory grade III proptosis with corneal dystrophy. The fundus was inaccessible. A computed tomography performed showed a sphenoid heterogeneous expansive process with left temporo-orbital extension with locoregional invasion. The child was referred to the pediatric neurosurgery department where the total tumor extraction was performed and the analysis of the surgical specimen revealed an orbito-temporal hamartoma.