Kimura’s disease an unusual cause of lymphadenopathy in a nephrotic syndrome child

Kimura’s disease is a rare, benign, chronic inflammatory disorder of unknown etiology which is endemic in Orientals. The disease is characterized by a triad of painless subcutaneous nodule in the head and neck region, blood eosinophilia and elevated serum immunoglobulin E (IgE) levels. Kimura’s disease has various synonyms such as eosinophilic lymphogranuloma, inflammatory angiomatous nodule and atypical pyogenic granuloma. Renal pathology such as nephrotic syndrome has been found to be associated with Kimura’s disease which states a common etiopathogenesis between renal lesion and Kimura’s disease. We present an eleven years old Malay boy with recurrent nephrotic syndrome presented with left post auricular swelling. The diagnosis was based on the characteristic histopathology findings after surgical biopsy as Kimura’s disease.