{"title":"强直性肌营养不良的呼吸管理","authors":"J. Bach, G. Chiarello","doi":"10.17352/aprc.000043","DOIUrl":null,"url":null,"abstract":"Patients with myotonic dystrophy can avoid episodes of respiratory failure by using up to continuous noninvasive ventilatory support (CNVS). Of 154 patients consecutively presenting to a neuromuscular disease clinic, 143 had types 1 or 2 and 11 had congenital myotonic dystrophy. Of the 76 who came multiple times, 41 were prescribed and used at least sleep NVS to relieve symptoms of fatigue and hypersomnolence.","PeriodicalId":167215,"journal":{"name":"Archives of Pulmonology and Respiratory Care","volume":"1 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2020-05-06","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Respiratory Management of Myotonic Dystrophy\",\"authors\":\"J. Bach, G. Chiarello\",\"doi\":\"10.17352/aprc.000043\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Patients with myotonic dystrophy can avoid episodes of respiratory failure by using up to continuous noninvasive ventilatory support (CNVS). Of 154 patients consecutively presenting to a neuromuscular disease clinic, 143 had types 1 or 2 and 11 had congenital myotonic dystrophy. Of the 76 who came multiple times, 41 were prescribed and used at least sleep NVS to relieve symptoms of fatigue and hypersomnolence.\",\"PeriodicalId\":167215,\"journal\":{\"name\":\"Archives of Pulmonology and Respiratory Care\",\"volume\":\"1 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2020-05-06\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Archives of Pulmonology and Respiratory Care\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.17352/aprc.000043\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Archives of Pulmonology and Respiratory Care","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.17352/aprc.000043","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Patients with myotonic dystrophy can avoid episodes of respiratory failure by using up to continuous noninvasive ventilatory support (CNVS). Of 154 patients consecutively presenting to a neuromuscular disease clinic, 143 had types 1 or 2 and 11 had congenital myotonic dystrophy. Of the 76 who came multiple times, 41 were prescribed and used at least sleep NVS to relieve symptoms of fatigue and hypersomnolence.
求助内容：
应助结果提醒方式：
京公网安备 11010802042870号
