{"title":"欧洲镰状细胞病儿童的管理:现状和未来展望","authors":"R. Colombatti, L. Sainati","doi":"10.33590/emjhematol/10310534","DOIUrl":null,"url":null,"abstract":"Sickle cell disease (SCD) is the most common haemoglobinopathy worldwide and its frequency has steadily increased in Europe in the past decades. SCD is a complex multisystem disorder characterised by chronic haemolytic anaemia, vaso-occlusive crisis, and vasculopathy. Clinical manifestations can be very different, ranging from mild haemolysis to life-threatening acute clinical complications and chronic disabilities. This review will explore service delivery across Europe to children with SCD, reporting on the available minimum standards of care and future perspectives.","PeriodicalId":326555,"journal":{"name":"EMJ Hematology","volume":"51 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2016-07-28","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"6","resultStr":"{\"title\":\"Management of Children With Sickle Cell Disease in Europe: Current Situation and Future Perspectives\",\"authors\":\"R. Colombatti, L. Sainati\",\"doi\":\"10.33590/emjhematol/10310534\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Sickle cell disease (SCD) is the most common haemoglobinopathy worldwide and its frequency has steadily increased in Europe in the past decades. SCD is a complex multisystem disorder characterised by chronic haemolytic anaemia, vaso-occlusive crisis, and vasculopathy. Clinical manifestations can be very different, ranging from mild haemolysis to life-threatening acute clinical complications and chronic disabilities. This review will explore service delivery across Europe to children with SCD, reporting on the available minimum standards of care and future perspectives.\",\"PeriodicalId\":326555,\"journal\":{\"name\":\"EMJ Hematology\",\"volume\":\"51 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2016-07-28\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"6\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"EMJ Hematology\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.33590/emjhematol/10310534\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"EMJ Hematology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.33590/emjhematol/10310534","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Management of Children With Sickle Cell Disease in Europe: Current Situation and Future Perspectives
Sickle cell disease (SCD) is the most common haemoglobinopathy worldwide and its frequency has steadily increased in Europe in the past decades. SCD is a complex multisystem disorder characterised by chronic haemolytic anaemia, vaso-occlusive crisis, and vasculopathy. Clinical manifestations can be very different, ranging from mild haemolysis to life-threatening acute clinical complications and chronic disabilities. This review will explore service delivery across Europe to children with SCD, reporting on the available minimum standards of care and future perspectives.