Rehabilitation of Non-Syndromic Oligodontia of Primary and Permanent Dentition in Young patient-A Rare Case Report

Background: Oligodontia is a genetic disorder which represents the congenital absence of more than six teeth in primary, permanent or both dentitions. It is usually a part of a syndrome and seldom occurs as an isolated entity. Genes responsible for non syndromic oligodontia are found to be MSX1 and PAX9 genes. Methods: Karyotyping was done taking sample from peripheral blood. Cytogenetic chromosome analysis revealed a normal male karyotype (46, XY) without any structural or numerical chromosome abnormalities. Hand wrists, clavicles, vertebral skeleton, skull and chest were found to be normal on radiological examination. After excluding other possible differential factors, the final diagnosis of non-syndromic Oligodontia was made. Preliminary impressions were made using impression compound and was molded on the edentulous ridge. Custom trays were fabricated and border molding was done using green stick impression compound and secondary impressions were made using zinc oxide eugenol impression paste. After maxillo-mandibular jaw relations, dentures were processed through compression molding technique. Dentures were inserted and the patient was taught about the insertion and removal of the dentures. Post insertion instructions regarding denture wear, functions of speech, mastication, hygiene and maintenance were given to the patient and the parent. Results: The patient was using prosthesis and happy with it during one year follow up. The rehabilitation with removable dentures at current age and later with osseo-integrated implants served as a satisfactory treatment outcome in such patients. Conclusion: This case report presents prosthodontic rehabilitation of a rare case of non-syndromic oligodontia in a 7-year old male patient with agenesis of all permanent teeth except the maxillary central incisors.