Congenital unilateral complete bony syngnathia with non-formation of TM joint and zygomatic arch disruption, Presenting at 11 years of age

Syngnathia refers to congenital adhesion of maxilla and mandible by fibrous or bony tissues with only 55 reported cases in literature. Occurrence of syngnathia with non-formation of temporo-mandibular joint (TMJ) in the absence of any other syndrome or congenital abnormality is a very rare presentation. An 11-year-old boy was presented with complaints of extreme degree limitation of mouth opening with left sided bony syngnathia, non-formation of left TMJ, and zygomatic arch disruption. The rarity of condition with non-definitive management options suggests a poor prognosis.