Bilateral Oculomotor Nerve Schwannomas Presenting With Ptosis And Occulomotor Nerve Palasy- A Rare Presentation Of Neurofibromatosis-2

Neurofibromatosis 2 (NF2) is a rare autosomal dominant disorder characterized by the development of multiple nervous system tumors. The presence of bilateral vestibular schwannomas is a defining feature, but patients with NF2 also develop other cranial, spinal, peripheral schwannomas, cranial and spinal meningiomas, and cataracts. Other associated intracranial lesions are non neoplastic calcifications with involvement of the Choroid plexus being most common. Cerebellar andcerebral cortical calcifications may also be seen .Though schwanomas other than 8th nerve schwannomas are known to occur but third nerve schwannomas are a rare presentation of NF-2.We at our institution report a rare case of bilateral occulomotor nerve schwannomas associted with massive 5th nerve schwannoma which presented with unilateral ptosis and third nerve palsy.