I. Haraki, S. ElYazal, A AitErrami, Lairani Fz, S. Jiddi, Z. Samlani, K. Krati, S. Oubaha
{"title":"两种罕见实体的不寻常关联:原发性直肠局限性炎和Klippel-Trenaunay综合征","authors":"I. Haraki, S. ElYazal, A AitErrami, Lairani Fz, S. Jiddi, Z. Samlani, K. Krati, S. Oubaha","doi":"10.17352/2455-2283.000059","DOIUrl":null,"url":null,"abstract":"Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder, characterized by the triad of vascular malformations (angioma), venous and or lymphatic malformations and asymmetrical disturbed growth of soft tissues and/or bone. Primary rectal linitis is a rare digestive tumor with very poor prognosis. We report the case of a 41-year-old patient with Klippel trenaunay syndrome who was diagnosed with primary rectal linitis.","PeriodicalId":422260,"journal":{"name":"Archives of Clinical Gastroenterology","volume":"69 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2019-01-17","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Unusual association of two rare entities: Primary rectal linitis and Klippel-Trenaunay syndrome\",\"authors\":\"I. Haraki, S. ElYazal, A AitErrami, Lairani Fz, S. Jiddi, Z. Samlani, K. Krati, S. Oubaha\",\"doi\":\"10.17352/2455-2283.000059\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder, characterized by the triad of vascular malformations (angioma), venous and or lymphatic malformations and asymmetrical disturbed growth of soft tissues and/or bone. Primary rectal linitis is a rare digestive tumor with very poor prognosis. We report the case of a 41-year-old patient with Klippel trenaunay syndrome who was diagnosed with primary rectal linitis.\",\"PeriodicalId\":422260,\"journal\":{\"name\":\"Archives of Clinical Gastroenterology\",\"volume\":\"69 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2019-01-17\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Archives of Clinical Gastroenterology\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.17352/2455-2283.000059\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Archives of Clinical Gastroenterology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.17352/2455-2283.000059","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Unusual association of two rare entities: Primary rectal linitis and Klippel-Trenaunay syndrome
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder, characterized by the triad of vascular malformations (angioma), venous and or lymphatic malformations and asymmetrical disturbed growth of soft tissues and/or bone. Primary rectal linitis is a rare digestive tumor with very poor prognosis. We report the case of a 41-year-old patient with Klippel trenaunay syndrome who was diagnosed with primary rectal linitis.