A Rare Case of Paratesticular Leiomyosarcoma

: INTRODUCTION: Para testicular leiomyosarcoma is very rare and standard treatment consists of radical orchiectomy and high cord ligation . The tumor usually presents with a painless, slow-growing scrotal mass in middle-aged or older men. 55 year old male patient with painless swelling in right side of scrotum since 4 months. Physical examination revealed a non -tender, solid mass on the right hemi-scrotum, measuring 15x5x3cms in diameter. Ultrasonogram of the scrotum opined right extratesticular mass. High inguinal orchidectomy done. Testis was appearing normal The pathological diagnosis was compatible with a paratesticular leiomyosarcoma Testicular parenchyma was normal with no significant pathology . On immunohistochemical staining, expression of SMA, muscle specific actin, and desmin was observed, while expression of CD34, S-100 protein, vimentin has been negative which confirms the diagnosis of leiomyosarcoma. CONCLUSION: The importance of presenting this paper is because of the rarity of the case and its confirmation by histopathology. oval