灾难性纤维肌肉发育不良伴有双侧肾梗死、椎动脉夹层和肠系膜缺血。

IF 0.7 Q4 UROLOGY & NEPHROLOGY
Nicholas Martin Gourd, Hannah Elizabeth Jenkins, Richard Miles, Adrienne Lee, Justin Mason, Andrew Connor
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引用次数: 0

摘要

纤维肌肉发育不良(FMD)是一种动脉壁肌肉层非动脉粥样硬化、非炎症性疾病,可导致动脉狭窄、闭塞和剥离。口蹄疫的临床表现因涉及的动脉区域而异,常常导致诊断困难。本病例报告描述了一个异常不寻常的FMD的表现,以前没有描述过,影响了一个以前健康和健康的37岁女性,表现为双侧肾梗死,连续椎动脉夹层,肠系膜缺血,需要继续肾脏替代。本报告强调了口蹄疫的不寻常表现如何掩盖了潜在的诊断。在鉴别诊断中早期考虑口蹄疫可以指导有效的管理策略,包括适当的影像学检查和多专业参与。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Catastrophic Fibromuscular Dysplasia Presenting with Concomitant Bilateral Renal Infarction, Vertebral Artery Dissection, and Mesenteric Ischaemia.

Catastrophic Fibromuscular Dysplasia Presenting with Concomitant Bilateral Renal Infarction, Vertebral Artery Dissection, and Mesenteric Ischaemia.

Catastrophic Fibromuscular Dysplasia Presenting with Concomitant Bilateral Renal Infarction, Vertebral Artery Dissection, and Mesenteric Ischaemia.

Catastrophic Fibromuscular Dysplasia Presenting with Concomitant Bilateral Renal Infarction, Vertebral Artery Dissection, and Mesenteric Ischaemia.

Fibromuscular dysplasia (FMD) is a non-atherosclerotic, non-inflammatory disorder of the arterial wall muscular layer which can lead to arterial stenosis, occlusion, and dissection. Clinical presentations of FMD vary depending on the arterial territories involved, often leading to diagnostic challenges. This case report describes an exceptionally unusual presentation of FMD, not previously described, affecting a previously fit and well 37-year-old female presenting with bilateral renal infarction, sequential vertebral artery dissections, mesenteric ischaemia, and the requirement for continued renal replacement. This report highlights how unusual presentations of FMD can mask the underlying diagnosis. Early consideration of FMD in a differential diagnosis can guide an effective management strategy, including appropriate imaging and multi-speciality involvement.

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来源期刊
CiteScore
1.20
自引率
0.00%
发文量
36
审稿时长
10 weeks
期刊介绍: This peer-reviewed online-only journal publishes original case reports covering the entire spectrum of nephrology and dialysis, including genetic susceptibility, clinical presentation, diagnosis, treatment or prevention, toxicities of therapy, critical care, supportive care, quality-of-life and survival issues. The journal will also accept case reports dealing with the use of novel technologies, both in the arena of diagnosis and treatment. Supplementary material is welcomed.
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