儿童成脂细胞瘤扩展至腰椎管1例报告。

IF 0.9 4区 医学 Q4 CLINICAL NEUROLOGY
Marina Saga, Akira Yamaura, Tadashi Miyagawa
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引用次数: 0

摘要

脂肪母细胞瘤和脂肪母细胞瘤病是罕见的良性间充质脂肪肿瘤,起源于胚胎白色脂肪细胞,最常见于婴儿期和幼儿期。成脂细胞瘤见于四肢和躯干,包括腹膜后和腹膜腔。因此,很少有关于脊髓管浸润的报道。病例介绍:一名四岁女童因难以伸直双腿坐在地板上而来到我们的诊所。她还主诉过去6个月的遗尿和便秘,并伴有持续性头痛和身体前屈引起的背痛。磁共振成像显示腰大肌、腹膜后和皮下间隙的巨大病变,延伸到L2和S1之间的脊髓硬膜外间隙。病人接受了手术,结果肿瘤从椎管中全部切除。肿块呈黄色,柔软,分叶状,脂肪多,易与周围组织分离。病理证实为脂肪母细胞瘤。术后过程很顺利,患者出院时没有任何神经功能障碍的迹象。结论:我们在此讨论一个罕见的病例,脂肪母细胞瘤延伸到椎管,导致神经系统症状。虽然这种肿瘤是良性的,没有转移的可能,但它很容易局部复发。因此,术后应密切观察。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Lipoblastomatosis Extended into the Lumbar Spinal Canal in a Child: A Case Report.

Introduction: Lipoblastoma and lipoblastomatosis are rare benign mesenchymal adipose tumors that originate from embryonic white adipocytes and occur most commonly in infancy and early childhood. Lipoblastomas occur in the extremities and trunk, including the retroperitoneum and peritoneal cavity. Therefore, infiltration into the spinal canal has rarely been reported.

Case presentation: A 4-year-old girl presented to our clinic because of difficulty sitting on the floor with her legs straight. She also complained of enuresis and constipation for the past 6 months with persistent headaches and back pain evoked by body anteflexion. A magnetic resonance imaging revealed a massive lesion of the psoas major muscle, retroperitoneal, and subcutaneous spaces, extending into the spinal epidural space between L2 and S1. The patient underwent surgery which resulted in gross total removal of the tumor from the spinal canal. The mass was yellowish, soft, lobulated, fatty, and easily removed from the surrounding structures. Pathology confirmed the diagnosis of lipoblastoma. The postoperative course was uneventful, and the patient was discharged without any signs of neurological deficit.

Conclusion: We herein discuss a rare case of lipoblastoma extending into the spinal canal, resulting in neurological symptoms. Although this tumor is benign with no potential for metastasis, it is prone to local recurrence. Therefore, close postoperative observation should be performed.

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来源期刊
Pediatric Neurosurgery
Pediatric Neurosurgery 医学-临床神经学
CiteScore
1.30
自引率
0.00%
发文量
45
审稿时长
>12 weeks
期刊介绍: Articles in ''Pediatric Neurosurgery'' strives to publish new information and observations in pediatric neurosurgery and the allied fields of neurology, neuroradiology and neuropathology as they relate to the etiology of neurologic diseases and the operative care of affected patients. In addition to experimental and clinical studies, the journal presents critical reviews which provide the reader with an update on selected topics as well as case histories and reports on advances in methodology and technique. This thought-provoking focus encourages dissemination of information from neurosurgeons and neuroscientists around the world that will be of interest to clinicians and researchers concerned with pediatric, congenital, and developmental diseases of the nervous system.
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