1例5岁患者球结膜丛状神经鞘瘤;期待意想不到的事情!

Mona Kenani, Rafaa Babgi, Sultan Bakri
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引用次数: 0

摘要

罕见的、不典型的成人眼科疾病包括球结膜丛状神经鞘瘤,它通常是无症状的。文献中很少有病例报告表明眼眶/结膜神经鞘瘤存在于成人患者中,很少在12岁以下儿童中。我们报告一例5岁的女孩谁提出了在门诊门诊颞下结膜非色素囊性病变10 × 10毫米的大小。经过检查,我们找不到喂食船。肿块可移动,未固定在巩膜上。病史显示持续1年,但左眼肿块在发病前2个月逐渐增大。无外伤或既往眼科手术史。手术成功切除囊肿,组织病理学检查证实了球结膜丛状神经鞘瘤的诊断。经定期随访评估,无复发或恶性转化的证据。虽然结膜神经鞘瘤在儿童中极为罕见,但在卵圆状边界清楚的眼眶肿胀中,特别是那些没有眼睛外伤或手术史的人,应考虑到这一点。手术切除是有效和安全的治疗干预。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Bulbar conjunctival plexiform schwannoma in a 5-year-old patient; expect the unexpected!

Bulbar conjunctival plexiform schwannoma in a 5-year-old patient; expect the unexpected!

Bulbar conjunctival plexiform schwannoma in a 5-year-old patient; expect the unexpected!

Rare, atypical ophthalmological conditions in adults include bulbar conjunctival plexiform schwannomas, which are usually asymptomatic. Few case reports in the literature indicate the presence of orbital/conjunctival schwannomas in adult patients and, rarely, among children under the age of 12. We report a case of a 5-year-old girl who presented in an outpatient clinic with inferior temporal conjunctival nonpigmented cystic lesion of a 10 × 10 mm size. Upon examination, we could not identify a feeding vessel. The mass was mobile and not fixed to the sclera. The history indicated a 1-year duration but the mass in the left eye had progressively increased in size during the last 2 months prior to presentation. There was no traumatic injury or past history of ophthalmic surgery. Surgical excision of the cyst was sucessfully performed, and histopathological examination confirmed bulbar conjunctival plexiform schwannoma diagnosis. Upon regular follow-up evaluation, there was no evidence of recurrence or malignant transformation. Although it is extremely rare to encounter conjunctival schwannomas in children, it should be considered in ovoidal well-circumscribed orbital swellings, particularly those that appear with no history of trauma or surgery to the eye. Surgical excision is effective and safe therapeutic intervention.

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