Efecan Cekic, Ahmet Karagoz, Mustafa Sakar, Rabia Emel Senay, Kadriye Ebru Akar, Suheyla Bozkurt, Adnan Dagcinar
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引用次数: 0
Abstract
Background: This is a case of aggressive Langerhans cell histiocytosis (LCH) with an atypical intracranial location.
Observations: In this report, the authors present the diagnosis and treatment of a 12-year-old male patient diagnosed with LCH. The patient was admitted to the emergency department with left-sided facial palsy, and a solid lesion with mass effect in the pons was found. A biopsy was performed via suboccipital craniotomy, and the diagnosis was LCH. A chemotherapy regimen was started since the LCH sample was the resistant type. The patient showed improvement in his neurological deficit following treatment.
Lessons: This rare localized and aggressive case's diagnosis process and treatment choices may apply to future cases.
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