Hypokalemic paralysis due to renal tubular acidosis: uncommon initial manifestation of primary Sjögren´s syndrome.

IF 1.4 4区 医学 Q3 RHEUMATOLOGY
ARP Rheumatology Pub Date : 2023-04-01
Margarida Correia, Carla Campinho Ferreia, Emanuel Costa, Diogo Esperança Almeida, Joana Leite Silva, Ana Roxo Ribeiro, Sofia Marques, Marcos Cerqueira
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引用次数: 0

Abstract

Primary Sjögren´s Syndrome is an immune-mediated disease characterized by exocrine glands dysfunction due to lymphoplasmacytic infiltration with sicca symptoms being one of its main features. The disease may, however, present as distal renal tubular acidosis due to renal involvement, which can range from asymptomatic to life-threatening. We describe the case of a 33-year-old woman with hypokalemic paralysis and metabolic acidosis secondary to distal renal tubular acidosis, leading to the diagnosis of primary Sjögren´s Syndrome. Although rare, recognizing primary Sjögren´s Syndrome as a possible cause of distal renal tubular acidosis may elicit an earlier diagnosis and treatment, improving the patient´s prognosis.

肾小管酸中毒所致低钾血症性麻痹:原发性Sjögren综合征的罕见初始表现。
原发性Sjögren综合征是一种免疫介导的疾病,以淋巴浆细胞浸润引起的外分泌腺功能障碍为特征,干燥症状是其主要特征之一。然而,由于肾脏受累,该病可能表现为远端肾小管酸中毒,其范围从无症状到危及生命。我们描述了一个33岁的女性低钾性麻痹和代谢性酸中毒继发于远端肾小管酸中毒,导致原发性Sjögren综合征的诊断。虽然罕见,但认识到原发性Sjögren’s综合征是远端肾小管酸中毒的可能原因可能会引起早期诊断和治疗,改善患者的预后。
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1.20
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