Right-sided high origin of diaphragm associated with accessory lobe of liver, lobulated right atrial appendage, and ipsilateral phrenic nerve hamartoma: a case report.

Abstract

A case of a rare condition of congenital right anterior high origin of the diaphragm in a stillborn fetus is reported. Associated findings at autopsy were a hornlike subdiaphragmatic intrathoracic accessory lobe of the liver and a lobulated right atrial appendage of the heart. At the superiormost aspect of the malpositioned right anterior diaphragmatic leaf a small phrenic nerve hamartoma was found. The phrenic nerve itself appeared small and not well developed. The phrenic nerve lesion may have been a concomitant or secondary hamartomatous change. Careful clinical and pathological search for concomitant anomalies in diaphragmatic lesions is emphasized.