Long term follow-up after the Ross procedure (RCD code: IV-5A.O)

Q4 Medicine

Journal of Rare Cardiovascular Diseases Pub Date : 2016-12-30 DOI:10.20418/JRCD.VOL3NO1.265

Aleksandra Lenart-Migdalska, Monika Smaś‑Suska, Klaudia Knap, M. Kaznica-Wiatr, M. Olszowska, P. Podolec, L. Tomkiewicz-Pajak

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Abstract

Aims: The aim of this study was to analyze the incidence of long-term complications observed during follow-up of patients who had undergone the Ross procedure in childhood. Methods: The study engaged a cohort of 9 patients, all of whom were between 19 to 32 years old. Patients had been in the care of the Centre for Rare Cardiovascular Diseases since the age of 18. Clinical and echocardiographic data were collected from the follow-up period. Results: 78% of patients had preserved global systolic function of the left ventricle, and 56% had dilatation of the ascending aorta. Due to the aneurysm of the ascending aorta one patient required the Bentall de Bono procedure. Another patient underwent a reoperation because of endocarditis of the pulmonary homograft with severe aortic and pulmonary regurgitation. 1/3 of the studied patients were being considered for a reoperation. 23% of patients developed severe pulmonary valve regurgitation, 33% moderate. 67% of patients developed mild to moderate pulmonary valve stenosis. Most patients were in NYHA class I-II. Conclusion: Late complications are frequent in this group of patients, and hence they require surveillance in specialized Centers for Grown-up Congenital Heart Diseases. JRCD 2016; 3 (1): 9–13

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罗斯手术后的长期随访(RCD代码:IV-5A.O)

目的:本研究的目的是分析在儿童时期接受Ross手术的患者随访期间观察到的长期并发症的发生率。方法:研究纳入9例患者，年龄均在19 ~ 32岁之间。病人自18岁以来一直在罕见心血管疾病中心接受治疗。在随访期间收集临床和超声心动图数据。结果:78%的患者左心室整体收缩功能保留，56%的患者升主动脉扩张。由于升主动脉动脉瘤，一名患者需要本特尔·德·博诺手术。另一名患者因肺同种移植物心内膜炎伴严重主动脉和肺反流而再次手术。三分之一的患者正在考虑再次手术。23%的患者出现重度肺瓣膜返流，33%为中度。67%的患者出现轻至中度肺动脉瓣狭窄。大多数患者为NYHA I-II级。结论:晚期并发症在这组患者中很常见，因此他们需要在成人先天性心脏病的专门中心进行监测。JRCD 2016;3 (1): 9-13

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来源期刊

Journal of Rare Cardiovascular Diseases Medicine-Cardiology and Cardiovascular Medicine

自引率

0.00%

发文量

审稿时长

23 weeks

期刊介绍： Journal of Rare Cardiovascular Diseases (JRCD) is an international, quarterly issued, peer-reviewed, open access, online journal that keeps cardiologists and non-cardiologists up-to-date with rare disorders of the heart and vessels. The Journal publishes fine quality review articles, original, basic and clinical sciences research papers, either positive or negative, case reports and articles on public health issues in the field of rare cardiovascular diseases and orphan cardiovascular drugs. Topics of interest include, but are not limited to the following areas: (1) rare diseases of systemic circulation (2) rare diseases of pulmonary circulation (3) rare diseases of the heart (cardiomyopathies) (4) rare congenital cardiovascular diseases (5) rare arrhythmogenic disorders (6) cardiac tumors and cardiovascular diseases in malignancy (7) cardiovascular diseases in pregnancy (8) basic science (9) quality of life