Anesthetic Management in Birt-Hogg-Dubé Syndrome with Spontaneous and Recurrent Pneumothorax during Recovery after Laparoscopic-Assisted Partial Nephrectomy

Abstract

Birt-Hogg-Dubé Syndrome (BHDS) is a hereditary condition associated with skin fibrofolliculomas, multiple lung cysts, and kidney tumors. We report a case of Birt-Hogg-Dubé Syndrome confirmed by folliculin (FLCN) genetic testing in a 45-year-old femalepatient with spontaneous and recurrent pneumothorax during recovery after laparoscopic-assisted partial nephrectomy.