A Custom-made Endovascular Treatment Strategy in a Patient with Marfan's Disease

Abstract

Introduction

We present a young female with Marfan's Syndrome and aortic dilatation between two previous dacron grafts of the descending thoracic and abdominal aorta after type B dissection.

Report

Open retrograde visceral revascularisation was undertaken and a single bespoke stent-graft used to exclude the aneurysm. A custom-made stent overcame some of the limitations of standard devices. A 50 mm proximal stent diameter was used to seal the landing zone in the dilated dacron thoracic graft.

Discussion

A single custom-made stent avoided multiple stent requirements to accommodate significant proximal/distal size discrepancy and reduced risk of type III endoleak in this young patient with complex disease.