Secuencia de Prune Belly: a propósito de un caso

Abstract

Background: The Prune-Belly sequence is a genetic disorder characterized by a triad that includes: weak abdominal wall musculature, urogenital anomalies, and bilateral cryptorchidism. Associated malformations usually accompany it. The surgical approach should be reserved for those patients with severe complications.Clinical case: We present a male neonate with agenesis of the abdominal wall musculature, multicystic renal dysplasia, and bilateral cryptorchidism, which is transferred from a primary hospital in eastern Ecuador and attended in conservative management during his hospitalization.Conclusions: The approach to SPB must be multidisciplinary due to its frequent association with other malformations. Prenatal diagnosis plays a fundamental role in the early detection of severe anomalies.