Cardiac transplantation for congenital long QT syndrome and recurrent sudden cardiac arrests despite automatic defibrillator implantation

Abstract

We report cardiac transplantation for congenital long QT syndrome in a patient who had recurrent cardiac arrests despite beta blockade, implantable cardioverter defibrillator and cervical sympathectomy. This is the first successful case of orthotopic transplantation for refractory cardiac arrhythmias in a patient with an otherwise normally functioning heart.