Acute Fatal Chest Pain: Spontaneous Massive Hemothorax in a Patient with Neurofibromatosis Type I

IF 0.3 4区医学 Q4 GERIATRICS & GERONTOLOGY

International Journal of Gerontology Pub Date : 2020-01-01 DOI:10.6890/IJGE.202008_14(3).0019

K. Hsu, Wenqun Huang, Chin-Wang Hsu, Yi-Chung Yu

引用次数: 0

Abstract

NF-1 is a genetic disorder with a rare incidence rate of approximately 1 in 3000. Arterial stenosis due to connective tissue dysplasia is a well-known vascular complication of NF-1, as well as aneurysms, which constitutes 3.6% of people diagnosed with this disease. Spontaneous hemothorax is one of the rare complications of NF-1. It is potentially fatal with a mortality rate as high as 36% and postoperative mortality of 33%. Massive and potentially fatal hemothorax caused by vascular complications is extremely uncommon. We present a rare case of massive hemothorax in a 62-year-old woman with NF-1 due to a spontaneous rupture of the right intercostal artery.

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急性致死性胸痛:1型神经纤维瘤病患者自发性大量血胸

NF-1是一种罕见的遗传性疾病，发病率约为1 / 3000。结缔组织发育不良引起的动脉狭窄是NF-1的一种众所周知的血管并发症，以及动脉瘤，占诊断为该疾病的患者的3.6%。自发性血胸是NF-1的罕见并发症之一。它具有潜在的致命性，死亡率高达36%，术后死亡率为33%。由血管并发症引起的大量且可能致命的血胸极为罕见。我们提出一个罕见的病例大量血胸62岁妇女NF-1由于自发破裂的右肋间动脉。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

International Journal of Gerontology 医学-老年医学

CiteScore

0.60

自引率

0.00%

发文量

审稿时长

6-12 weeks

期刊介绍： The Journal aims to publish original research and review papers on all fields of geriatrics and gerontology, including those dealing with critical care and emergency medicine. The IJGE aims to explore and clarify the medical science and philosophy in all fields of geriatrics and gerontology, including those in the emergency and critical care medicine. The IJGE is determined not only to be a professional journal in gerontology, but also a leading source of information for the developing field of geriatric emergency and critical care medicine. It is a pioneer in Asia. Topics in the IJGE cover the advancement of diagnosis and management in urgent, serious and chronic intractable diseases in later life, preventive medicine, long-term care of disability, ethical issues in the diseased elderly and biochemistry, cell biology, endocrinology, molecular biology, pharmacology, physiology and protein chemistry involving diseases associated with age. We did not limit the territory to only critical or emergency condition inasmuch as chronic diseases are frequently brought about by inappropriate management of acute problems.