Challenges in the diagnosis and management of a patient with von Willebrand's disease in a resource-limited setting; A case report of a 7-year-old boy with massive cephal-hematoma

Abstract

von Willebrand disease (vWD) is the commonest inherited bleeding disorder. In Nigeria like many other developing countries, there are only a few documented patients with this condition. This low number of patients with vWD in our setting is multifactorial; including lack of a high index of suspicion among clinicians, lack of diagnostic facilities, and unavailability of blood products and/or desmopressin used in treating bleeding episodes in these patients among others. We present a 7-year-old boy who presented to our facility with massive cephal-hematoma following trauma.