Scimitar syndrome – a case report

IF 0.1 Q4 OBSTETRICS & GYNECOLOGY

Case Reports in Perinatal Medicine Pub Date : 2021-01-01 DOI:10.1515/crpm-2020-0088

L. Sá, T. Pereira, Ana B. Ferreira, A. Reis, A. Madureira, Margarida Azevedo

引用次数: 0

Abstract

Abstract Objectives The aim of this article is to describe a clinical case of Scimitar syndrome, an unusual cause of respiratory distress in the neonatal period. This syndrome is a rare form of partial or total anomalous right lung venous drainage to the inferior caval vein, usually associated with right pulmonary hypoplasia. Case presentation The authors report a case of a 36-week-old newborn admitted to the neonatal intensive care unit with worsening respiratory distress. Chest radiography revealed a characteristic right pulmonary hypoplasia and a tubular structure paralleling the right heart border in the shape of a Turkish sword (“scimitar”). Chest computed tomography angiography confirmed the diagnosis. Conclusions Age of presentation and the severe malformations found, contributed to the patient’s poor outcome in this case.

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弯刀综合症-个案报告

摘要目的本文的目的是描述一个临床病例的弯刀综合征，呼吸窘迫在新生儿时期的一个不寻常的原因。该综合征是一种罕见的右肺静脉部分或全部异常引流至下腔静脉的症状，通常伴有右肺发育不全。病例介绍作者报告了一个病例36周大的新生儿入院新生儿重症监护病房恶化呼吸窘迫。胸片示特征性右肺发育不全，与右心边界平行的管状结构，呈土耳其刀状。胸部计算机断层血管造影证实了诊断。结论本例患者的发病年龄及所发现的严重畸形是导致预后不良的主要原因。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Case Reports in Perinatal Medicine OBSTETRICS & GYNECOLOGY-

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期刊介绍： Case Reports in Perinatal Medicine is a double-blind peer-reviewed journal. The objective of the new journal is very similar to that of JPM. In addition to evidence-based studies, practitioners in clinical practice esteem especially exemplary reports of cases that reveal specific manifestations of diseases, its progress or its treatment. We consider case reports and series to be brief reports describing an isolated clinical case or a small number of cases. They may describe new or uncommon diagnoses, unusual outcomes or prognosis, new or infrequently used therapies and side effects of therapy not usually discovered in clinical trials. They represent the basic concept of experiences for studies on representative groups for further evidence-based research. The potential roles of case reports and case series are: Recognition and description of new diseases Detection of drug side effects (adverse or beneficial) Study of mechanisms of disease Medical education and audit Recognition of rare manifestations of disease.

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