Limb Salvage Treatment of Large Multicentric Extra-Abdominal Desmoid Tumor of Lower Extremity

Abstract

Aggressive fibromatoses or desmoid tumor (DT) is a very rare soft tissue neoplasms with incidence 2 – 4 cases per billion every year [1]. Fibromatoses is fibroblast origin benign tumor lesion, locally invasive but never metastatic and with high recurrence rate [2]. There are two types of DT – superficial and the deep group. The deep group is divided into extra abdominal, intra-abdominal and abdominal type and all of them are histologically similar [1]. Extra abdominal presentation is the rarest type and usually tumor is located on head and neck [3], chest wall [4] and spinal cord [5]. Limb localization is most often found in the upper extremity shoulder and arm region, and in lower extremity buttocks, back of the thigh and knee joint [6-8]. So far, the literature describes only several cases of anterior lower limb presentation of desmoid tumor, one case presentation in bilateral lower limbs and there are no literature findings of ipsilateral knee and ankle joint presentation (Table 1) [7-10]. Volume 8 Issue 6 2017