The maxillonasal dysplasia

Abstract

Maxillonasal dysplasia also called Binder’s syndrome is a congenital deformity characterized by nasomaxillary hypoplasia that is attributed to underdeveloped mid-facial skeleton (1). They have a characteristic appearance that is effortlessly identifiable (2). Binder, who first defined this syndrome as a distinct clinical entity in 1962, attributed the cause of this syndrome to the disturbance of the prosencephalic induction center during embryonic life (3). Noyes in 1939 described the salient features of Binder’s syndrome (4). Binder reported 3 cases and presented 6 characteristic features for this syndrome (5). Arhinoid face, abnormal position of the nasal bones, intermaxillary hypoplasia with consecutive malocclusion, reduced or absent anterior nasal spine, atrophy of the nasal mucosa and absence of the frontal sinus.