The recovery from dilated cardiomyopathy followed by hypertrophic cardiomyopathy, in the course of deficiency of long-chain 3-hydroxyacyl- coenzyme A dehydrogenase in infant

J. Kwiatkowska, Julita Świtońska, J. Wierzba
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引用次数: 1

Abstract

Dilated cardiomyopathy is one of the most common causes of the heart failure in childhood and can develop as a consequence of metabolic disorders such as fatty acid beta-oxidation disorders or amino acids metabolism disorders. In our report we present a case where in the course of deficiency of long-chain 3-hydroxyacyl-coenzyme A dehydrogenase the recovery from dilated cardiomyopathy resulted in hypertrophic cardiomyopathy.
婴儿长链3-羟基酰基辅酶A脱氢酶缺乏过程中扩张型心肌病后肥厚型心肌病的恢复
扩张型心肌病是儿童期心衰最常见的原因之一,可发展为代谢紊乱的结果,如脂肪酸-氧化障碍或氨基酸代谢紊乱。在我们的报告中,我们提出了一个病例,在长链3-羟基酰基辅酶a脱氢酶缺乏的过程中,扩张型心肌病的恢复导致肥厚性心肌病。
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