A Rare Cause of Pituitary Deficiency: Pituitary Stalk Interruption Syndrome and Magnetic Resonance Imaging Findings

FORBES Pub Date : 2020-01-01 DOI:10.5222/forbes.2020.24008
Ahmet Hikmet Çilengir, F. C. Sarıoğlu, N. Çilengir, B. Dirim Mete
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引用次数: 0

Abstract

Pituitary stalk interruption syndrome is a rare disease characterized by a deficiency of adenohypophyseal hormones. Clinical presentation usually occurs in childhood or in the second decade of life. The severity of hormonal deficiency is variable. It may be isolated or be accompanied by extra–pituitary anomalies. Magnetic resonance imaging findings are considered as an absent pituitary stalk, absent or smaller adenohypophysis, absent or ectopic neurohypophysis. Contrast-enhanced imaging is essential in evaluating the presence and morphology of the pituitary stalk. In the presence of clinical findings, evaluation of the hypothalamic–pituitary region using magnetic resonance imaging is necessary for diagnosis. Early diagnosed cases can maintain their normal lives with hormone replacement. In this article, we aimed to present pituitary stalk interruption syndrome and its magnetic resonance imaging findings with a case presentation
垂体缺乏的一种罕见病因:垂体柄中断综合征和磁共振成像结果
垂体柄中断综合征是一种罕见的疾病,其特征是腺垂体激素缺乏。临床表现通常发生在童年或生命的第二个十年。激素缺乏的严重程度是不同的。它可能是孤立的或伴有垂体外异常。磁共振成像表现为垂体柄缺失,腺垂体缺失或较小,神经垂体缺失或异位。对比增强成像在评估垂体柄的存在和形态是必不可少的。在临床表现,评估下丘脑-垂体区使用磁共振成像是必要的诊断。早期诊断的病例可以通过激素替代维持正常生活。在这篇文章中,我们的目的是提出垂体柄中断综合征及其磁共振成像的表现与一个病例的报告
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
FORBES
FORBES BUSINESS, FINANCE-
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