Extramedullary Myeloidsarcoma in Children Presenting with Pancreatic Tumor

Abstract

Background: Myeloidsarcoma (MS) is a tumor composed of granulocytic precursor cells occurring in an extramedullary location.MS are rare neoplasms whose knowledge is largely based on case reports. MS is often initially misdiagnosed, the most common alternative diagnoses being lymphoma, undifferentiated cancer, malignant melanoma, extramedullary hematopoiesis and inflammation. Immunohistochemistry and immunophenotying are crucial for the accurate diagnosis of MS. Aim: The aim of this study is to introduce a boy with a very rare clinical case of MS in the diagnosis of myelodysplastic syndrome. Case report: A 9-year-old boy with extramedullary MS has been treated in Pediatric Oncology Department, K hospital from May, 2016 to August, 2016. Method: Retrospectively describe a clinical case. Result: The patient is described smilar to some other cases in literature. He was treated with an Acute Myeloicytic Leukemia conventional chemotherapeutic protocol and discharged. Conclusion: The case is rare in clinical practice. The exact diagnosis was made by immunohistochemistry and immunophenotying. Treatment with systemic chemotherapy was associated with his primary favorable survival outcome.