Mixoma mandibular en paciente de 3 años, una entidad específica. Tratamiento quirúrgico conservador. Caso clínico y revisión de la literatura

Abstract

The odontogenic myxoma or myxofibroma (OM), is considered within the group of benign tumors with mesenchyme with or without odontogenic epithelium. It represents about 3-9░% of all odontogenic tumors, with an incidence of 0.07/1,000,000 inhabitants per year. The third decade is the most prevalent, with greater incidence in women than men, having a predilection in the posterior region of the jaw. This tumor has slow growth and is locally aggressive, without presenting symptoms in most cases. The standard surgical treatment according to the literature is resection with safety margin. However, there are reports of conservative treatments (enucleation and curettage) in young pediatric patients with low recurrence rates. The purpose of this case report is to present a 3-year-old male patient with an MO in the body area of the jaw, treated with complete hysteresis of the lesion plus perilesional curettage. Clinical and radiographic follow-up was performed at 2, 4 and 10 months post surgery, then annually until 5 years post surgery without signs of recurrence. According to publications regarding the MO in children, it is pointed out that this should be considered a unique pathology due to its clinical characteristics different from those of the adult and the report of low recurrence rate with conservative surgical treatments. Whereas the literature regarding pediatric OM is not abundant. The fact that background information is provided regarding a rare location and a conservative treatment without relapse of the MO in a 3-year-old patient and with 5 years of follow-up, allows to deliver a hope of non-aggressive surgeries in future pediatric patients under 4 years old with OM