PATHOLOGY TEACH AND TELL: CENTRAL NERVOUS SYSTEM ATYPICAL TERATOID/RHABDOID TUMOR

Abstract

Atypical teratoid/rhabdoid tumor (AT/RT) is extremely malignant, highly aggressive primitive central nervous systemneoplasm of infancy with very poor prognosis. Histologically, AT/RT is defined as a polymorphous neoplasm often featuring rhabdoid, PNET, mesenchymal, and epithelial components. We report the clinical history, radioligical, and pathological findings in a child affected bycentral nervous system AT/RT.