Hipertensión arterial pulmonar en paciente con neumonía intersticial no específica y con test de vasorreactividad positivo

Abstract

Pulmonary hypertension (PH) is a disease characterized by a progressive increase of pulmonary vascular resistance, which gives rise to right ventricular failure and premature death. This may be idiopathic or be associated to different conditions, standing out among them collagen, toxic diseases and lung conditions such as interstitial lung diseases.

We present the case of a female patient diagnosed of PH with images suggestive of interstitial disease in the high resolution computed tomography and who was subsequently diagnosed of a non-specific interstitial pneumonia. It is important to stress the positive vasoreactivity test in cardiac catheterization that may indicate the presence of two independent conditions in the present case.