Anesthetic management of a child with methylmalonic acidemia for lens aspiration – a case report

Abstract

We report a case of a child with methylmalonic acidemia who presented to our hospital for lens aspiration surgery. Methylmalonic acidemia is an inherited disorder of protein catabolism. Its clinical effects can vary from mild to severe, and include lethargy, vomiting, hypotonia, hypothermia, failure to thrive and encephalopathy. The main concern in treatment of these patients is prevention of academia by identifying precipitating factors. It is especially important to acutely manage fluids and electrolytes before, during and after surgery.