Paediatric Pulmonary hypertension

Abstract

in pa ti ents with idiopathic PAH, the available results suggest bene fi cial e ff ects of these new treatments in this popula ti on as well. The lack of data on long-term e ff ects, however, makes op ti mal ti ming of drug therapy speci fi cally in pa ti ents with PAH and CHD di ffi cult. Limited studies in children suggest bene fi cial short-term e ff ects, comparable to adults. Further research, including larger clinical trials with long term follow up, is needed for the development of an evidence based treatment algorithm tailored for adults and children with the heterogeneous presenta ti ons of PAH associated with CHD.