Bilateral lens coloboma in child with Marfan's syndrome treated with lens surgery

Abstract

Lens coloboma can occur with ocular or systemic associations like Marfan's and Stickler's syndrome. Causes of poor vision include refractive error, anisometropia and amblyopia. Visual rehabilitation and surgery is technically challenging in these patients. Here we report a child with progressive defective vision with Marfans syndrome and lens coloboma who underwent successful surgery with intraocular lens (IOL) placement. The bag was stabilised with capsule tension ring and iris hooks, and the IOL was further stabilised with optic capture. Postoperatively, the child regained good vision in the operated eye with very good centration of the IOL at three month follow up visit.