Multifocal, biatrial, primary cardiac embryonal rhabdomyosarcoma.

IF 2.5 Q2 OBSTETRICS & GYNECOLOGY
Przeglad Menopauzalny Pub Date : 2023-09-01 Epub Date: 2023-09-25 DOI:10.5114/pm.2023.131459
Ioannis Panagiotopoulos, Anastasia Katinioti, Vasileios Mousafeiris, Vasileios Leivaditis, Konstantinos Skevis, Konstantinos Tasios, Andreas Antzoulas, Christos Pitros, Georgios-Ioannis Verras, Francesk Mulita, Sotirios Prapas
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引用次数: 0

Abstract

Malignant primary cardiac tumors are rare, with atrial myxoma and rhabdomyosarcoma the common types in adult and pediatric populations respectively. Rhabdomyosarcomas are rare and are usually located in the atria; they present with symptomatology dependent on their location. A 63-year-old woman presented with the symptomatology of dyspnea, cough, and palpitations and was diagnosed with biatrial primary cardiac rhabdomyosarcoma, which required excision. The postoperative course was uneventful and the patient was discharged on the 5th postoperative day. Postoperative cardiac functional tests revealed an ejection fraction of 60%, consistent with the preoperative value, and no mitral valve dysfunction. Biatrial rhabdomyosarcomas are extremely rare, with only 3 cases reported, including ours, reported in the literature, to the best of our knowledge. Transthoracic echocardiogram is useful in the diagnosis. They require surgical excision along with chemotherapy or radiotherapy. Their prognosis is poor, with a median survival of almost one year. Primary biatrial rhabdomyosarcoma is an extremely rare diagnosis that can present with symptomatology based on the location, size, and number of masses. There is no consensus on how to manage them due to the scarcity of cases, but they are managed as single rhabdomyosarcomas. The majority require surgical excision, with subsequent chemotherapy or radiotherapy. The prognosis is very poor, with the majority of the patients not surviving longer than one year.

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多灶、双试验、原发性心脏胚胎性横纹肌肉瘤。
原发性心脏恶性肿瘤很少见,心房粘液瘤和横纹肌肉瘤分别是成人和儿童人群的常见类型。横纹肌肉瘤是罕见的,通常位于心房;他们的症状取决于他们的位置。一名63岁的女性出现呼吸困难、咳嗽和心悸的症状,被诊断为双试验原发性心脏横纹肌肉瘤,需要切除。术后进展顺利,患者于术后第5天出院。术后心功能检查显示射血分数为60%,与术前值一致,无二尖瓣功能障碍。双发性横纹肌肉瘤极为罕见,据我们所知,只有3例报告,包括我们的病例,在文献中报道。经胸超声心动图可用于诊断。它们需要手术切除,同时进行化疗或放疗。他们的预后很差,中位生存期几乎为一年。原发性双发性横纹肌肉瘤是一种极为罕见的诊断,可根据肿块的位置、大小和数量表现出症状。由于病例稀少,关于如何治疗还没有达成共识,但它们是作为单一的横纹肌肉瘤来治疗的。大多数需要手术切除,随后进行化疗或放疗。预后非常差,大多数患者的存活时间不超过一年。
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来源期刊
Przeglad Menopauzalny
Przeglad Menopauzalny OBSTETRICS & GYNECOLOGY-
CiteScore
3.40
自引率
11.10%
发文量
32
审稿时长
6-12 weeks
期刊介绍: Menopausal Review is a scientific bimonthly aimed at gynecologists and endocrinologists.
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