Percutaneous occlusion of five pulmonary arteriovenous fistulas in the same pulmonary lobe.

Abstract

Hereditary hemorrhagic telangiectasia (HHT) or Osler Weber Rendu Syndrome (OWRS) is a multiorgan disorder, of autosomal dominant inheritance, resulting in fibrovascular dysplasia with multiple arteriovenous malformations in different organs1. Pulmonary arteriovenous malformations are the most common pulmonary findings found in patients with HHT2,3. They can be asymptomatic or may present various symptoms such as cyanosis, dyspnea, heart failure, hemoptysis, and paradoxical embolism4.