Arrhythmogenic right ventricular cardiomyopathy.

Abstract

Arrhythmogenic right ventricular cardiomyopathy is a cardiac disorder manifested by the replacement of the ventricular myocardium by fibro fatty tissue and has been known to cause sudden cardiac death in young adults. In 30% to 50% of cases, the disease has familial links, which can have implications for the patients and families involved. Achieving a diagnosis can be taxing on all involved, and for the patient, it can mean having to go through a battery of tests. Once diagnosis has been confirmed, treatment for the disease includes implantation of an implantable defibrillator and/or pharmacotherapy to control the ventricular tachyarrhythmias.