Transcatheter therapy of Budd-Chiari syndrome in a child after liver transplantation: report of one case.

Chi-Lin Ho, Yun-Ching Fu, Chieh-Chung Lin, Shao-Bin Cheng, Sheng-Ling Jan, Ming-Chih Lin, Ching-Shiang Chi, Betau Hwang
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Abstract

Budd-Chiari syndrome is a rare, heterogenous and potentially lethal condition due to hepatic venous outflow obstruction. Classic triads include hepatomegaly, ascites and abdominal pain. Most cases are caused by abnormal coagulopathy, infection, inflammation or tumor invasion. Status post liver transplantation was rarely mentioned in the pediatric group. Here we report a case of 4-year-old girl with biliary atresia status post living donor liver transplantation. Marked ascites developed 2 months later and Budd-Chiari syndrome was diagnosed. Cardiac catheterization showed significant stenoses of the hepatic vein and inferior vena cava. Initial balloon angioplasty of inferior vena cava only resulted in mild improvement. After successful balloon angioplasty of the hepatic vein stenosis, the stenosis of the inferior vena cava improved significantly. The ascites resolved soon, and no more happened up to 8 months' follow-up.

经导管治疗儿童肝移植术后Budd-Chiari综合征1例报告。
Budd-Chiari综合征是一种罕见的,异质性和潜在的致命疾病,由肝静脉流出梗阻引起。典型的三联征包括肝肿大、腹水和腹痛。大多数病例是由凝血功能异常、感染、炎症或肿瘤侵袭引起的。肝移植后的状态在儿科组中很少被提及。我们在此报告一例4岁女童在活体肝移植后出现胆道闭锁的情况。2个月后出现明显腹水,诊断为Budd-Chiari综合征。心导管检查显示肝静脉及下腔静脉明显狭窄。最初的下腔静脉球囊成形术只导致轻微的改善。肝静脉球囊成形术成功后,下腔静脉狭窄明显改善。腹水很快消失,随访8个月无再次发生。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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