Neurilemmoma of the diaphragm causing severe hypertrophic pulmonary osteoarthropathy

Abstract

• 1.

  One case of primary neurilemmoma of the left leaf of the diaphragm occurring in a girl aged 5 is described. This brings the total number of primary neurogenic tumours of the diaphragm in the literature to six. This is the second case of neurilemmoma.

• 2.

  The presenting feature of this case was severe hypertrophic pulmonary osteoarthropathy. This has occurred in half the cases reported.

• 3.

  The removal of the tumour led to rapid improvement in the osteoarthropathy.

• 4.

  The importance of early operative treatment is emphasised because of the high incidence of malignancy.