H M Barragán-Campos, C F Barrera-Ramírez, P Iturralde Torres, H Ilarraza-Lomelí, M C Avila-Casado, B Estañol, J Dorantes, J Oseguera
{"title":"Kearns-Sayre syndromes an absolute indication for prophylactic implantation of definitive pacemaker?","authors":"H M Barragán-Campos, C F Barrera-Ramírez, P Iturralde Torres, H Ilarraza-Lomelí, M C Avila-Casado, B Estañol, J Dorantes, J Oseguera","doi":"","DOIUrl":null,"url":null,"abstract":"<p><p>Kearns-Sayre syndrome is a mitochondrial cytopathy characterized by chronic progressive external ophthalmoplegia, retinitis pigmentosa and heart block, the last of which determines the survival of these patients. The case of a 23 year old man with Kearns-Sayre syndrome, conduction disturbances and mitral valve prolapse is presented. The characteristics of this syndrome are described and the criteria for prophylactic installation of a pacemaker discussed.</p>","PeriodicalId":75556,"journal":{"name":"Archivos del Instituto de Cardiologia de Mexico","volume":"69 6","pages":"559-65"},"PeriodicalIF":0.0000,"publicationDate":"1999-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Archivos del Instituto de Cardiologia de Mexico","FirstCategoryId":"1085","ListUrlMain":"","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0
Abstract
Kearns-Sayre syndrome is a mitochondrial cytopathy characterized by chronic progressive external ophthalmoplegia, retinitis pigmentosa and heart block, the last of which determines the survival of these patients. The case of a 23 year old man with Kearns-Sayre syndrome, conduction disturbances and mitral valve prolapse is presented. The characteristics of this syndrome are described and the criteria for prophylactic installation of a pacemaker discussed.