Bentall Procedure in a Patient with Loeys-Dietz Syndrome: A Case Report.

IF 1.4 Q3 ANESTHESIOLOGY

Annals of Cardiac Anaesthesia Pub Date : 2026-10-01 Epub Date: 2026-10-12 DOI:10.4103/aca.aca_317_25

Dheeraj Arora, Supriya Chaudhary, Rajesh Madavathazathil Gopalakrishnan, Sameer Bhate

引用次数: 0

Abstract

Abstract: Loeys-Dietz syndrome (LDS) is a rare autosomal dominant connective tissue disorder characterized by aggressive aortopathy, craniofacial anomalies and systemic involvement. Rapid aortic root dilatation and valvular dysfunction mandate an early surgical intervention. We report a case of 15-year-old boy with LDS, rapidly progressive aortic root dilatation and severe aortic regurgitation (AR) who underwent successful Bentall procedure. The case highlights the need of early detection, multidisciplinary involvement and meticulous anesthetic care.

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本特尔手术治疗Loeys-Dietz综合征1例报告。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Annals of Cardiac Anaesthesia ANESTHESIOLOGY-

CiteScore

1.60

自引率

0.00%

发文量

147

审稿时长

26 weeks

期刊介绍： Annals of Cardiac Anaesthesia (ACA) is the official journal of the Indian Association of Cardiovascular Thoracic Anaesthesiologists. The journal is indexed with PubMed/MEDLINE, Excerpta Medica/EMBASE, IndMed and MedInd. The journal’s full text is online at www.annals.in. With the aim of faster and better dissemination of knowledge, we will be publishing articles ‘Ahead of Print’ immediately on acceptance. In addition, the journal would allow free access (Open Access) to its contents, which is likely to attract more readers and citations to articles published in ACA. Authors do not have to pay for submission, processing or publication of articles in ACA.