Atypical Dilated and Nonhypertrophic Cardiac Transthyretin Amyloidosis: Concept of Overlapping Cardiomyopathies

CASE (Philadelphia, Pa.) Pub Date : 2026-09-01 Epub Date: 2026-07-08 DOI:10.1016/j.case.2026.04.009
Louis Simard MD MSc, Christian-Yves Couture MD, MSc, Joëlle Morin MD, Mathieu Bernier MD, Kim O'Connor MD, Erwan Salaun MD, PhD
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引用次数: 0

Abstract

  • •
    Subtle age-related ATTR-CM can complicate preexisting other HF etiologies.
  • •
    Combined cardiomyopathies can present with atypical clinical/imaging presentation.
  • •
    Multimodal imaging assessment is required in overlapping cardiomyopathies.
  • •
    Absence of myocardial thickening should not rule out an infiltrative disorder.
  • •
    Endomyocardial biopsy remains important in the context of equivocal imaging.
  1. Download: Download high-res image (285KB)
  2. Download: Download full-size image
非典型扩张型和非肥厚型心脏转甲状腺素淀粉样变性:重叠型心肌病的概念
•微妙的年龄相关性atr - cm可使先前存在的其他HF病因复杂化。•合并心肌病可表现为不典型的临床/影像学表现。•重叠心肌病需要多模式成像评估。•心肌没有增厚不应排除浸润性疾病。•在影像不明确的情况下,心内膜活检仍然很重要。下载:下载高清图片(285KB)下载:下载全尺寸图片
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来源期刊
CASE (Philadelphia, Pa.)
CASE (Philadelphia, Pa.) Radiology and Imaging, Cardiology and Cardiovascular Medicine, Radiography
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