{"title":"Balancing Risks in Obstetrics: Anesthesia Management in Facioscapulohumeral Muscular Dystrophy with Scoliosis.","authors":"Ashwin Mani, Sukriti Jha, Vinay Kumar, Shailendra Kumar","doi":"10.70278/AANAJ/.0000001035","DOIUrl":null,"url":null,"abstract":"<p><p>Facioscapulohumeral muscular dystrophy (FSHD), the third most common form of muscular dystrophy, is associated with a normal life expectancy, resulting in more pregnant women presenting with the condition. Pregnancy often exacerbates muscle weakness in patients with FSHD, posing unique perioperative challenges. Careful evaluation of systemic involvement is essential to minimize maternal and neonatal risks. Perioperative management is often challenging because both general and neuraxial anesthesia carry significant risks. Spinal deformities further complicate anesthesia management, requiring troubleshooting. Apart from these challenges, literature on managing FSHD during cesarean sections is limited. We report the successful anesthetic management of an elective cesarean section in a patient with FSHD and scoliosis, reviewing troubleshooting measures for neuraxial blocks in spinal deformities.</p>","PeriodicalId":7104,"journal":{"name":"AANA journal","volume":"93 5","pages":"371-374"},"PeriodicalIF":0.0000,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"AANA journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.70278/AANAJ/.0000001035","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"Medicine","Score":null,"Total":0}
引用次数: 0
Abstract
Facioscapulohumeral muscular dystrophy (FSHD), the third most common form of muscular dystrophy, is associated with a normal life expectancy, resulting in more pregnant women presenting with the condition. Pregnancy often exacerbates muscle weakness in patients with FSHD, posing unique perioperative challenges. Careful evaluation of systemic involvement is essential to minimize maternal and neonatal risks. Perioperative management is often challenging because both general and neuraxial anesthesia carry significant risks. Spinal deformities further complicate anesthesia management, requiring troubleshooting. Apart from these challenges, literature on managing FSHD during cesarean sections is limited. We report the successful anesthetic management of an elective cesarean section in a patient with FSHD and scoliosis, reviewing troubleshooting measures for neuraxial blocks in spinal deformities.
期刊介绍：
Founded in 1931 and located in Park Ridge, Ill., the AANA is the professional organization for more than 90 percent of the nation’s nurse anesthetists. As advanced practice nurses, CRNAs administer approximately 32 million anesthetics in the United States each year. CRNAs practice in every setting where anesthesia is available and are the sole anesthesia providers in more than two-thirds of all rural hospitals. They administer every type of anesthetic, and provide care for every type of surgery or procedure, from open heart to cataract to pain management.
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