A Prenatally Diagnosed Rare Vascular Ring Formed by Left Aortic Arch and Right Ductus Arteriosus

Q4 Medicine

JACC. Case reports Pub Date : 2025-10-08 DOI:10.1016/j.jaccas.2025.105275

Nana Matsuzawa MD, PhD , Yuka Yamamoto MD, PhD , Eri Kitamura MD, PhD , Yuri Ishida MD, PhD , Jun Takeda MD, PhD , Noboru Tanaka MD, PhD , Lisa K. Hornberger MD , Atsuo Itakura MD, PhD

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Abstract

Background

A vascular ring arises during the development of the fetal arches and is often associated with a double aortic arch or right-sided aorta, an aberrant left subclavian artery with a posterior esophageal component, and a left-sided ductus arteriosus.

Case Summary

This is a rare vascular ring formed by a left aortic arch, aberrant right subclavian artery, and right ductus arteriosus that was diagnosed prenatally by fetal echocardiography. The 3-vessels and trachea (3VT) view with 2-dimensional and color Doppler sweeps were helpful in defining the vascular pathology. Tracheomalacia was also noted, and genetic tests confirmed the presence of 22q11.2 deletion.

Discussion

The distal portions of the right sixth and right eighth dorsal arches were persistent, whereas the right fourth and distal part of the left sixth arches disappeared in the process of fetal development.

Take-Home Message

Use of the 3VT echocardiography sweep facilitates prenatal diagnosis of rare vascular rings.

查看原文本刊更多论文

由左主动脉弓和右动脉导管形成的罕见的产前诊断血管环。

背景：在胎儿弓发育过程中出现血管环，通常与双主动脉弓或右侧主动脉、具有食管后成分的左侧锁骨下动脉异常和左侧动脉导管相关。病例总结：这是一种罕见的血管环，由左主动脉弓、异常的右锁骨下动脉和右动脉导管组成，产前通过胎儿超声心动图诊断。三血管及气管（3VT）的二维和彩色多普勒扫描有助于确定血管病理。气管软化症也被发现，基因测试证实存在22q11.2缺失。讨论：右第六和右第八背弓远端部分是持久的，而右第四和左第六背弓远端部分在胎儿发育过程中消失。带回家的信息：使用3VT超声心动图扫描有助于产前诊断罕见的血管环。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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